Arrhythmogenic Right Ventricular Cardiomyopathy

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Arrhythmogenic Right Ventricular Cardiomyopathy is the second most common cause of sudden cardiac death in young people after hypertrophic cardiomyopathy. It is characterized electrocardiographically by T-wave inversions in the right precordial leads (V1-V3) and an Epsilon wave – a small deflection after the QRS complex usually best seen in V1-V3.

Examples

ECG Showing Arrhythmogenic Right Ventricular Cardiomyopathy

Arrhythmogenic Right Ventricular Cardiomyopathy

This ECG was obtained in a young patient that presented with syncope. Notice the presence of an epsilon wave in V1 - a specific finding for this diagnosis - and T-wave inversions in the precordial leads. Cardiac MRI confirmed fatty infiltration of the right ventricle.

References